ABSTRACT
Synovial sarcomas are most frequently observed in the extremities. A lthough synovial sarcomas are the third most common histological type of soft-tissue sarcomas of the extremities, primary mediastinal synovial sarcoma is extremely rare. Monophasic synovial sarcoma is the most commonly observed subtype. whereas the biphasic subtype is less common. We present our case which was diagnosed as biphasic synovial sarcoma located in the anterior mediastinum, which is considered to be a rare entity. The patient underwent surgical resection together with multimodal adjuvant radiotherapy and chemotherapy
Subject(s)
Humans , Female , Adult , Sarcoma, Synovial/surgery , Sarcoma, Synovial/radiotherapy , Sarcoma, Synovial/therapy , Mediastinal Neoplasms , Antineoplastic AgentsABSTRACT
Esse relato apresenta o caso de uma paciente com quarta recidiva de sinoviosarcoma, um sarcoma de partes moles que possui estreita relação com bainhas tendinosas, bursas e cápsulas articulares. A paciente apresentou uma quarta recidiva, sendo necessária a realização da amputação de perna, visto que as cirurgias conservadoras já não aliviam o sofrimento da paciente. O principal objetivo deste relato de caso é apresentar um caso clássico de neoplasia rara, expondo a doença e fazer uma breve revisão da literatura e mostrar sua importância, visto que corresponde a apenas 5% das neoplasias de partes moles.
This report presents the case of a female patient with fourth synoviosarcoma recurrence, a sarcoma of soft parts that have close relationship with tendom sheaths, bursas and articular capsule.The patient present her fourth recurrence, in wich the perfomance of amputation was required, since the conservative surgeriesno longer relieved the patient suffering. The main objective of this case report is to present a classic case of a rare cancer, exposing the disease, and to make a brief review of the literature to show its importance, since it corresponds to only five percent of the cancers of soft parts.
Subject(s)
Humans , Female , Adult , Sarcoma, Synovial/diagnosis , Sarcoma, Synovial/therapy , Ankle/pathology , Amputation, Surgical , Soft Tissue Neoplasms/diagnosis , Soft Tissue Neoplasms/therapy , Prognosis , Neoplasm Recurrence, Local , Treatment OutcomeSubject(s)
Humans , Female , Sarcoma, Synovial/diagnosis , Sarcoma, Synovial/therapy , Immunohistochemistry , Child , Recurrence , ReviewABSTRACT
Os autores apresentam um caso de sinoviossarcoma na coxa direita de paciente jovem, do sexo feminino, precedido por episódio de trombose venosa femoral, onde, apesar de conduta adequada e em tempo hábil, a evoluçäo näo foi boa, surgindo metástase pélvica, seis meses após o diagnóstico. Descrevem a conduta diagnóstica e a terapêutica adotada, discutindo-a bem como tecem consideraçöes sobre os sarcomas de partes moles em geral, com base na literatura